A Case of Chronic Inflammatory Demyelinating Polyneuropathy Associated with Transient Abducens Nerve Palsy |
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Abstract |
Chronic inflammatory demyelinating polyneuropathy (CIDP) with cranial nerve involvement has been rarely reported. A 27-year-old female suddenly developed diplopia for 4 days. Her past history disclosed relapse-remitting pattern of motor weakness and sensory impairment for 5 years. A transient diplopia during unknown period was developed 5 years ago. Recently, she had aggravation of motor weakness after postpartum 2 months ago. Neurological examination and electrophysiological study showed sensorimotor polyneuropathy of demyelinating type, and left 6th cranial nerve palsy. Brain MRI showed no abnormality, and laboratory studies including autoimmune, metabolic, and monoclonal antibodies were all normal. The left 6th nerve palsy disappeared spontaneously after 1 week without treatment, and limb weakness and sensory change were partially responded to steroid treatment. |
Key Words:
Chronic inflammatory demyelinating polyneuropathy (CIDP), Cranial nerve, Abducens nerve |
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