Monomelic Amyotrophy - Report of Nine Cases -

J Korean Assoc EMG Electrodiagn Med 2000;2(1):49-54.
Published online May 9, 2000.

Abstract

We reviewed the clinical, electrophysiological, and radiological findings in 9 patients with monomelic amyotrophy. Monomelic amyotrophy is a rare form of motor neuron disease usually presenting as painless asymmetric weakness and atrophy in the distal upper extremities of young males. Most cases are sporadic. Symptoms and signs often progress for several years before spontaneously arrested Laboratory testing is frequently normal or nonspecific except for electrophysiological studies. The results of electrophysiological, radiological, and the muscle biopsy findings suggest chronic anterior horn cell disease. Although the prevalence of this disease is still unknown, the importance of recognition is being emphasized because of its common occurrence in our country and the benign course and good prognosis.

Key Words: Monomelic amyotrophy, Motor neuron disease